摘要
Rokitansky-Kuster-Hauser综合征为副中肾管发育障碍所致,主要表现为先天性无阴道、始基子宫,女性第二性征、外生殖器、输卵管、卵巢均正常。本文报道20例RKH综合征,阴道及子宫均发育不良甚致缺如,第二性征均为女性型。其中8例进行气腹造影见卵巢未见子宫影;2例腹腔镜检查也见卵巢,未见子宫;4例剖腹探查发现2例未发育双子宫、1例未发育单子宫、1例未见子宫,均见卵巢,其中1例卵巢增大病理诊断为无性细胞瘤。8例静脉肾盂造影有2例显示肾畸形。本文对RKH综合征的胚胎发生以及与其它先天性无阴道疾病的鉴别诊断加以讨论。
Twenty-six cases of the agenesis of vagina were admitted during 1956—1932.Among them 20 cases were of Rokitansky-Küster-Hauser(RKH)syndrome,diagnosed by laparoscopy in 2,pelvic pneumography in 8,laparotomy in 4 and the remaining 6 by physical examination.In addition to the absence of vagina,the uterus was absent or rudimentary.The ovaries were all normal in size,except one with an ovarian tumor.Abnormal urinary system was found in 2 out of 8 patients by intravenous pyelography,absence of the right kidney in one and ectopic right kidney in the other.Theembryognesis of RKH syndrome and differential diagnosis of the agenesis of vagina are discussed.
出处
《上海医学》
CAS
1983年第9期528-532,共5页
Shanghai Medical Journal
