摘要
目的了解噬血细胞综合征的临床特点,治疗及预后。方法分析22例噬血细胞综合征患儿的临床资料。结果临床表现为持续发热,肝脾淋巴结肿大,2系以上外周血细胞减少,肝功异常,凝血障碍,低纤维蛋白血症,高甘油三脂血症,骨髓涂片或淋巴结活检有增多的噬血细胞。结论噬血细胞综合征临床表现凶险,对高度怀疑为噬血细胞综合征的患者,应及早干预治疗,改善预后。
Objectives understand clinic charactaristics,therapy and prognosis of hemophagocytic syndrome.Methord analyse clinic data of the patients of the hemophagocytic syndrome.Result The clinic sign have long fever,hepatomegaly,splenomegaly,lymphadenovarix,blood cell reduced,liver unfunction,thrombin unfunction,low-fibrinogen and high-trinitroglycerin.there are more hemophagocytes in bone marrow or in lymphaden.Conclusion hemophagocytic syndrome is a kind of dangerous disease,we should early diagnose and cure the;...
出处
《中国病案》
2009年第2期49-50,共2页
Chinese Medical Record
关键词
噬血细胞综合征
诊断
治疗
hemophagocytic syndrome
diagnosis
therapy
