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女性假两性畸形影像表现 被引量:5

Imaging features of female pseudohermaphroditism
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摘要 目的 评价女性假两性畸形的影像学特点。方法 回顾性分析 9例女性假两性畸形的影像资料。结果  7例未经激素治疗者 ,双侧肾上腺内外支一致性增粗、延长、扭曲 ,其中 2例呈结节状、肿块状 ;2例长期补充激素者中 ,1例肾上腺延长但不增粗 ,另 1例与未治疗者相仿 ,且有髓质瘤形成 ;4例有子宫、卵巢发育不良。结论 女性假两性畸形为遗传性疾病 ,其肾上腺增生、内生殖器官发育不良为继发性 ,影像学检查可早期发现 ,如及早治疗 ,上述改变可望恢复正常。 Objective To evaluate the imaging features of female pseudohermaphroditism. Methods The imaging findings in 9 cases of female pseudohermaphroditism were analyzed retrospectively.Results Thickening, prolongation, and twist of bilateral adrenal glands was found in 7 untreated cases, 2 of them had macronodular hyperplasia.One of the treated cases was without thickening or twist of adrenal glands, the other treated case coexisted with adrenal myelolipoma.Agenesis of the uterus and vagina was found in 4 cases.Conclusion Female pseudohermaphroditism is a hereditary disease, and the hyperplasia of adrenal glands and agenesis of uterus and vagina were secondary manifestations.Early detection of these abnormalities could be achieved with imaging modalities, and early treatment could result in remedy of these abnormalities.
出处 《中华放射学杂志》 CAS CSCD 北大核心 2005年第1期64-66,共3页 Chinese Journal of Radiology
关键词 女性假两性畸形 影像表现 肾上腺 早治疗 双侧 早期发现 肿块 恢复 一致性 延长 Female pseudohermaphroditism Adrenal hyperplasia, congenital Diagnostic imaging
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共引文献16

同被引文献34

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