摘要
报道2003～2006年发现的3例原发性血色病患者，3例均为男性，有典型皮肤色素沉着、糖尿病、肝肿大；血清铁蛋白明显升高，分别为1414．7μg／L、902μg／L、1063．4μg／L。2例有心功能衰竭，性功能减低。3例均行腹部CT检查，肝脏CT值均明显增强。例1行去铁铵及双重滤过血浆置换治疗后，血清铁蛋白由1414．7μg降为245μg／L，例2死于心功能衰竭，例3行放血治疗血清铁蛋白由1063．4μg／L降为556．0μg／L。
3 cases of primary （hereditory） hemochromatosis were found from 2003 to 2006. They were male and had typical pigmentation, diabetes, hepatomegaly with marked increase of plasma ferritin to 1414. 7 μg /L ,902 μg/L, 1063.4μg/L respectively. Two patients had heart failure and sexual hypofunetion. The liver showed homogenous high density in all 3 cases. One of them died of heart failure. Others were treated effectively by venesection , deferoxamine and double superfiltered plasma displacement respectively.
出处
《中国实用医药》
2009年第25期71-73,共3页
China Practical Medicine
关键词
原发性血色病
血清铁蛋白
Primary hemochromatosis
Plasma ferritin
