摘要
目的探讨肝脏血管周上皮样细胞瘤(PEComa)的临床特点和诊治原则。方法回顾性分析2010年1月~2018年12月收治的8例肝脏血管周上皮样细胞瘤的临床资料,对肝脏PEComa的临床特点、影像学表现、病理结果、治疗及预后进行分析。结果8例病人中肝脏单发肿瘤4例,多发3例,肝肾多发1例。其中4例行肝右叶肿瘤切除术,3例行肝左叶肿瘤切除术,1例行双侧肝叶肿瘤切除术。手术时间180~310分钟,平均(255.0±15.7)分钟,术中出血量100~400 ml,平均(258.8±32.6)ml。8例均经病理证实为PEComa。术后随访均未见复发。结论肝脏PEComa是一种相对罕见的肝脏肿瘤,以良性为主,确诊依赖于术后病理学检查。主要治疗措施是手术切除,预后良好。
Objective To elucidate the the clinical features,and the principles in diagnosis and treatment of hepatic perivascular epithelioid cell tumor(PEComa).Methods The clinical data of 8 cases with PEComas from January,2010 to December 2018,were studied.We analyzed the clinical characters,imaging manifestation,treatment and prognosis of these cases with hepatic PEComa.Results Among the 8 patients,4 had single liver tumor,3 had multiple liver and kidney tumors,and 1 had multiple liver and kidney tumors.Four patients underwent right lobe tumor resection,three underwent left lobe tumor resection,and one underwent bilateral lobe tumor resection.Operation time was 180-310 min,average(255.0±15.7)min,peroperative bleeding was 100-400 ml,average(258.8±32.6)ml.All the 8 cases were confirmed as PEComa by pathology.Postoperative follow-up showed no recurrence.Conclusion Hepatic PEComa is a relatively rare liver tumor,which is definitively diagnozed by post-operative pathological examination.Surgical resection is an optimal therapy for hepatic PEComa.The major of hepatic PEComa is benign tumor,so the prognosis is relatively well.
作者
罗鸿萍
龙新
张磊
LUO Hongping;LONG Xin;ZHANG Lei(Hepatic Surgery Center,Tongji Hospital,Tongji Medical College,Huazhong University of Science and Technology,Wuhan 430030,China)
出处
《临床外科杂志》
2019年第8期659-660,共2页
Journal of Clinical Surgery
基金
卫生部重大疾病专项资助项目(2008ZX10002-025)
卫生部部属医院临床学科重点资助项目(2007-353)
湖北省肝脏外科医学研究中心资助项目
关键词
血管周上皮样细胞瘤
免疫组织化学
外科治疗
预后
perivascular epithelioid cell tumor
immunohistochemistry
surgical treatment
prognosis
