摘要
白塞综合征是一种病因未明的全身慢性血管炎症性疾病,临床表现多样,且缺乏特异性实验室指标,临床误诊和漏诊率较高。中华医学会风湿病学分会在借鉴国内外诊治经验和指南的基础上,制定了本诊疗规范,旨在规范白塞综合征诊断及各系统受累的治疗策略,减少误诊漏诊及严重不良事件的发生,改善患者预后。
Behçet′s syndrome(BS)is classified among variable vessel vasculitis with unknown etiology and extensively heterogeneous clinical features.It is easily missed or misdiagnosed due to the lack of a specific laboratory diagnosis index.Based on the evidence and guidelines from China and other countries,the Chinese Rheumatology Association developed the standardization of diagnosis and treatment of BS.The purposes are:(1)To standardize the detection and interpretation of key indicators for BS;(2)To standardize rational management for BS patients with topical and systemic organ involvement to reduce complications and improve outcomes.
作者
郑文洁
张娜
朱小春
池淑红
张文
魏蔚
赵岩
董怡
Zheng Wenjie;Zhang Na;Zhu Xiaochun;Chi Shuhong;Zhang Wen;Wei Wei;Zhao Yan;Dong Yi(Department of Rheumatology and Clinical Immunology,Peking Union Medical College,Peking Union Medical College Hospital,Chinese Academy of Medical Sciences,National Clinical Research Center for Dermatologic and Immunologic Diseases,Ministry of Science&Technology,State Key Laboratory of Complex Severe and Rare Diseases,Key Laboratory of Rheumatology and Clinical Immunology,Ministry of Education,Beijing 100730,China;Department of Rheumatology and Clinical Immunology,Tianjin Medical University General Hospital,Tianjin 300052,China;Department of Rheumatology,the First Affiliated Hospital of Wenzhou Medical University,Wenzhou 325000,China;Department of Rheumatology,General Hospital of Ningxia Medical University,Yinchuan 750004,China)
出处
《中华内科杂志》
CAS
CSCD
北大核心
2021年第10期860-867,共8页
Chinese Journal of Internal Medicine